Abstract: Background: Hirschsprung disease is a congenital disorder characterized by the absence of ganglion cells in the Meissner plexus (submucosa) and Auerbach plexus (muscularis) which extend for varying distances proximally. Hirschsprung disease can occur in 1:5000 births. The aim of this study was to determine the Association between functional outcomes and the quality of life in Hirschsprung patients after pulltrough at Dr. M. Djamil General Hospital.
Methods: This study was an analytical descriptive study with a cross sectional approach in patients Hirschprung's disease after pullthrough in 2023, whose functional outcomes were evaluated using the Krickenbeck classification questionnaire and quality of life using the PedsQL questionnaire. The subjects selected for this study were patients diagnosed with Hirschsprung who underwent Pulltrough surgery at Dr. M. Djamil General Hospital, has sufficient data in medical records, is ?3 years old, can still be contacted, and is willing to be included in the research.
Results: The research sample was 22 (55%) men and 18 (45%) women. With 87.5% of patients having voluntary bowel movements, 12.5% did not experience voluntary bowel movements. There are 2.5% of patients who cannot feel the urge to defecate (soiling) every day, 15% of patients who experience soiling once or twice a week and 82.5% of patients who do not soil. 2 patients (5%) had constipation that required laxatives, 6 patients (15%) had constipation that could be managed with diet and 32 patients (80%) did not experience constipation. There were 8 patients with physical function disorders (20%), 12 patients with emotional function disorders (30%), 7 patients (17.5%) with social function disorders and 0 patients (0%) with school function disorders.
Conclusion: There is a significant association between the functional outcomes of Hirschsprung patients and the quality of life patients after pull through.
